Proteus syndrome with syringohydromyelia and arachnoid cyst

ANIK Y. , Anik İ. , Gonullu E., Inan N., Demirci A.

CHILDS NERVOUS SYSTEM, vol.23, no.10, pp.1199-1202, 2007 (Journal Indexed in SCI) identifier identifier identifier

  • Publication Type: Article / Article
  • Volume: 23 Issue: 10
  • Publication Date: 2007
  • Doi Number: 10.1007/s00381-007-0364-z
  • Title of Journal : CHILDS NERVOUS SYSTEM
  • Page Numbers: pp.1199-1202


Introduction Proteus syndrome (PS) is a rarely seen, sporadic disorder with a wide range of abnormalities including asymmetrical overgrowth, skin lesions, dysregulated adipose tissue, and vascular malformations. Brain and spinal malformations are extremely rare; syringohydromyelia and arachnoid cyst have not been reported previously.