ALCAPA Syndrome and Atrial Septal Defect In a 68-Year-Old Woman: An Extremely Rare Congenital Association

Cankurt T., Acar B., Aydin S., Maden O.

ACTA CARDIOLOGICA SINICA, vol.33, no.4, pp.447-449, 2017 (SCI-Expanded) identifier identifier identifier

  • Publication Type: Article / Article
  • Volume: 33 Issue: 4
  • Publication Date: 2017
  • Doi Number: 10.6515/acs20160608c
  • Journal Indexes: Science Citation Index Expanded (SCI-EXPANDED), Scopus
  • Page Numbers: pp.447-449
  • Keywords: ALCAPA, Atrial septal defect, Congenital cardiac defect, Coronary anomaly, WHITE-GARLAND-SYNDROME
  • Kocaeli University Affiliated: Yes


Anomalous left coronary artery arising from the pulmonary artery (ALCAPA) has been generally reported as an isolated lesion that is also called Bland-White-Garland syndrome. Herein we report a case of ALCAPA syndrome with an atrial septal defect in a 68-year-old woman. She had been asymptomatic until the age of 68. Echocardiographic examination revealed atrial septal defect, and coronary angiography showed that the left main coronary artery originated from the pulmonary artery and intensive collateral connections between the right and left coronary artery. In this case, it would appear that ALCAPA is associated with atrial septal defect.