Akademik Veri Yönetim Sistemi
Pediatric Cardiology, 2026 (SCI-Expanded, Scopus)
Accessory mitral valve tissue is a congenital cardiac anomaly that can lead to left ventricular outflow tract obstruction. Although it is predominantly diagnosed in pediatric populations, true incidence remains unknown but is considered rare, and clinical recognition can be challenging. With the widespread use of echocardiography, this anomaly is being diagnosed more frequently. This retrospective study was conducted on patients diagnosed with accessory mitral valve tissue between April 2010 and August 2025. Accessory mitral valve tissue was identified in 47 patients (17 females, 30 males) with a mean age at diagnosis of 121 ± 53.2 months. The most common indication for echocardiographic evaluation was murmur (n = 15). Additional congenital heart defects were observed in 18 patients (38%). The most frequent associated anomaly was bicuspid aortic valve (n = 6, 13%). Left ventricular outflow tract obstruction was noted in 6 patients with accessory mitral valve tissue. Two patients underwent surgical resection of accessory mitral valve tissue; one due to subaortic obstruction and the other due to mitral valve stenosis. Concomitant congenital heart diseases mainly from left-sided heart structures are frequently seen. Left ventricular outflow tract obstruction and aortic regurgitation owing to accessory mitral valve tissue may gradually increase during follow-up. Cardiac surgery may be necessary in patients with left ventricular outflow tract obstruction or aortic regurgitation. Echocardiography is the cornerstone for the initial diagnosis, serial follow-up, and management guidance of patients with this condition.